VACTERL association with Prune-Belly syndrome.
نویسندگان
چکیده
We report a term, small for gestational age neonate having full spectrum of VACTERL association. In addition, the neonate also had triad of signs and symptoms associated with prune belly syndrome. The concurrence of these two syndromes could lie in their common etiology of defect in mesodermal differentiation. Such a combination is extremely rare and is generally incompatible with life.
منابع مشابه
It's not All Doom and Gloom: Prune Belly Syndrome Associated with VACTERL
Prune belly syndrome is a rare abnormality; its association with VACTERL is even rarer. This association has been reported in literature a few times since first reported in 1993 and so far the majority have either been stillbirths or died shortly after birth. We present a case of Prune belly syndrome associated with VACTERL who is now one year old.
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ورودعنوان ژورنال:
- Indian pediatrics
دوره 41 8 شماره
صفحات -
تاریخ انتشار 2004